862 Successful Surgical Management of Chylothorax Secondary to Gorham-Stout Disease
نویسندگان
چکیده
Abstract Introduction Gorham-Scout Disease (GSD) is a rare skeletal disorder of unknown aetiology characterised by progressive osteolysis and excessive lymphovascular proliferation. Chylothorax severe life-threatening complication GSD that confers poor prognosis. Literature review reveals only one previous case successful surgical management for chylothorax secondary to GSD. Case presentation A teenage asylum seeker presented with large left pleural effusion on background chronic flank collection malformation. Cytological analysis the fluid drained from chest drain insertion confirmed chylothorax. posterior rib excision biopsy helped confirm diagnosis She had VATS ligation thoracic duct talc pleurodesis, however, due recollection ongoing symptomatic discomfort, she subsequently underwent thoracotomy, decortication lung pleurectomy. These interventions stabilise related radiotherapy pain control via administration bisphosphonates. Conclusions disease can develop number complications including Management radiotherapeutic techniques provide long term remission, other modalities may be needed in order optimise analgesic requirements.
منابع مشابه
Erratum: Pregnancy Complicated by Gorham–Stout Disease and Refractory Chylothorax
[This corrects the article DOI: 10.1055/s-0036-1593443.].
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Introduction Gorham-Stout Disease (GSD) is a rare disorder of bony destruction due to lymphangiomatosis, and is often triggered by hormones. One complication of GSD is the development of chylothorax, which carries a high mortality rate. Very little experience has been published to guide management in GSD during pregnancy to optimize both fetal and maternal health. Case Study A 20-year-old woman...
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Gorham-Stout Disease (GSD) is a rare lymphatic disorder affecting children or young adults with no predilection of sex. It is generally associated with vanishing bone osteolytic lesions, thoracic and abdominal involvement, and diffuse pulmonary lymphangiomatosis. Chylous effusions and chylothorax, consequent to the abnormal proliferation of lymphatic vessels, may induce respiratory failure with...
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RATIONALE Gorham-Stout disease (GSD) is characterized by aggressive bone resorption, proliferation of vascular or lymphatic vessels, and soft-tissue swelling. Bones that initially appear normal start to resorb, partially or completely. However, the etiology of GSD is unknown. PATIENT CONCERNS A 29-year-old man with a chief complaint of toothache and mobility in the lower right mandible for th...
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ژورنال
عنوان ژورنال: British Journal of Surgery
سال: 2023
ISSN: ['1365-2168', '0007-1323']
DOI: https://doi.org/10.1093/bjs/znad258.291